International Journal of Academic Health and Medical Research (IJAHMR)   Year: 2022 | Volume: 6 | Issue: 5 | Page No.: 74-78 Dermoid Cyst of the Posterior Cerebral Fossa Associated with A Congenital Dermal Sinus in A Child: Download PDF Chaymae Hajjar , Mariyem Ferhi, Meriem Haloua, Nizar El Bouardi , Badreeddine Alami, Moulay Youssef Alaoui Lamrani,Mustapha Maaroufi, Meriem Boubbou . Abstract: The dermoid cyst of the central nervous system is a very rare entity. It is a benign tumor that can be associated with dysraphic disorders, mainly in the dermal sinus. Hydrocephalus and surinfection are the main complications of the dermoid cyst of the posterior cerebral fossa. Neuroradiological examinations (especially CT and MRI) are necessary for diagnosis, followed later by anatomopathological confirmation. The curative treatment is surgical. We present a case of a 04-year-old child, without any notable pathological history, who was consulted for acute isolated intracranial hypertension, with a cerebral CT showing an obstructive hydrocephalus that complicates a dermoid cyst of the posterior cerebral fossa associated with an occipital dermal sinus. Purpose: Consider the posterior dermoid cerebral fossa cyst in children with a median cystic lesion on sectional imaging, especially if it is associated with a complete or incomplete occipital dermal sinus.