International Journal of Academic Health and Medical Research (IJAHMR)   Year: 2023 | Volume: 7 | Issue: 3 | Page No.: 89-92 Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome: A case report and review of the literature Download PDF K.Bouras, K.Laouini, M. K. Saoud, N. Mamouni, S.Errarhay, C. Bouchikhi, A. Banani Abstract: Mayer-Rokitansky-Kuster-Hauser syndrome is a rare embryopathy characterised by a congenital absence of the uterus and the upper 1/3 of the vagina. It may be isolated or associated with other malformations, notably kidney and bone. The treatment consists of conservative treatment by progressive dilatation of the vagina. Currently 3D printing of personalised vaginal mould offre an excellent result. Sometimes surgical reconstruction of a neo vagina is used. We report the case of a 26-year-old patient with Mayer-Rokitansky-Kuster-Hauser syndrome, and provide an updated review of the literature.