Title: Prenatal Diagnosis of Complex Double-Outlet Right Ventricle Associated with Atrioventricular Canal Defect : A Case Report Case Report
Authors: Benchaaboune Kenza, Hekmat Chaara, Tazi Zineb, Belhaj Yassine, Jayi Sofia, Fdili Alaoui FZ, My Abdel Illah Melhouf
Volume: 10
Issue: 7
Pages: 80-84
Publication Date: 2026/07/28
Abstract:
Double-outlet right ventricle (DORV) is a rare congenital cardiac malformation in which both great arteries arise predominantly from the morphological right ventricle. Its antenatal diagnosis requires careful segmental analysis of the fetal heart and precise assessment of the ventriculoarterial connections. We report the case of a 19-year-old primigravida referred at 38 weeks and 3 days of gestation for delivery planning after antenatal suspicion of complex congenital heart disease. The pregnancy was complicated by severe fetal growth restriction and severe preeclampsia. Antenatal ultrasound showed ventricular septal defect, ventricular imbalance, malposition of the great arteries with suspected origin from the right ventricle, an anterior aorta, a posterior pulmonary artery, and a narrow subpulmonary pathway suggestive of pulmonary stenosis. Cesarean delivery was performed for maternal rescue after persistent severe hypertension despite medical management. Postnatal transthoracic echocardiography confirmed complex DORV associated with atrioventricular canal defect, right ventricular dominance, moderately hypoplastic left ventricle, and valvular and supravalvular pulmonary stenosis. This case underlines the value of prenatal ultrasound in complex conotruncal anomalies and highlights the importance of multidisciplinary perinatal planning and postnatal echocardiographic confirmation.